• Users Online: 221
  • Home
  • Print this page
  • Email this page
Home About us Editorial board Search Ahead of print Current issue Archives Submit article Instructions Subscribe Contacts Login 
CASE REPORT
Year : 2016  |  Volume : 6  |  Issue : 1  |  Page : 35-39

Orodental manifestations of enamel renal syndrome in siblings: A rare case report


1 Department of Oral Medicine and Radiology, Subharti Dental College and Hospital, Meerut, Uttar Pradesh, India
2 Department of Oral Pathology and Microbiology, Subharti Dental College and Hospital, Meerut, Uttar Pradesh, India

Correspondence Address:
Jyoti Sharma
Department of Oral Medicine and Radiology, Subharti Dental College and Hospital, Meerut, Uttar Pradesh
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/2231-6027.186665

Rights and Permissions

Amelogenesis imperfecta (AI) is a group of hereditary disorders that affect the quality and/or quantity of dental enamel. Hypoplastic AI can occur per se or in a variety of ectodermal syndromes and metabolic disorders. Enamel renal syndrome (ERS) is a very rare disorder associating hypoplastic AI with nephrocalcinosis. Since nephrocalcinosis is often asymptomatic, the orodental findings and dental radiographic features play a key role in the diagnosis of this extremely rare inherited disorder. This paper describes the orodental manifestations of ERS in siblings who were born of consanguineous parents.


[FULL TEXT] [PDF]*
Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed1932    
    Printed17    
    Emailed0    
    PDF Downloaded127    
    Comments [Add]    

Recommend this journal